Erythrokeratodermia Variabilis with Rare Associations in a Child: A Case Report

Abstract

Erythrokeratodermia variabilis (EKV) or Mendes da Costa disease is a genomic ailment transmitted as an autosomal dominant trait. EKV presents with two distinctive skin lesions which comprises well demarcated, fixed, figurate hyperkeratotic plaques and transient erythematous patches which typically presents at birth or initial infancy. We report a case on Erythrokeratodermia variabilis in a child who presented with grievances of erythematous raised lesions with scaling over the abdomen, back, extremities with left side clubfoot deformity.